Total Dysfunction 25 (43.86) 10 (21.74) 37.90 (1.86, 15.36) 4.62, 0.03\*
Low Function 22 (39.29) 7 (15.22) 36.10 (1.79, 14.27) 4.38, 0.04\*
Borderline 12 (21.05) 8 (16.33) 12.90 (1.12, 14.68) 2.19, 0.15
Abnormal 7 (12.28) 10 (21.28) 14.05 (1.34, 13.69) 2.52, 0.10
Disease Severity:
Severe 20 (35.09) 11 (23.40) 15.10 (1.42, 14.76) 3.02, 0.08
Borderline 12 (21.05) 8 (16.33) 12.90 (1.12, 14.68) 2.19, 0.15
Mild 25 (43.86) 27 (56.25) 33.33 (2.04, 11.65) 4.61, 0.03\*
Normal 4 (7.02) 4 (8.20) 12.50 (0.44, 14.55) 1.16, 0.34
FSHD: The scores range from 1 to 5, with 5 meaning no limitation and 1 meaning an extreme limitation in daily living activities.
######
Comparison of mean scores on the two versions of the CST-QOL by diagnosis of FSHD
-----------------------------------------------------------------------------------------------------------------------------
*Total number*\ Units Adult version of the CST-QOL Child version of the CST-QOL *t* P value
*of cases*
------------------------------------------ -------- ------- ---------------------------- ----------------------------- ------- --------- -----------
All patients (39) Mean 12.10 10.75 -1.35 -4.05 0.0001\*
S.D ± 3.86 ± 3.69 *t* = -3.65, 0.001\*\*
Mild (20) Mean 13.18 8.93 -4.25 -6.21 0.0001\*
S.D ± 3.70 ± 4.35 *t* = -4.25, 0.001\*\*
Normal (17) Mean 8.24 10.34 1.14 -1.01 0.33
*P* value for t-test of equality of means\*
N Mean S.D
Total Dysfunction(21) 25 5.48 3.55
Low Function (17) 22 5.36 3.31
Borderline (11) 12 6.00 3.64
Abnormal (7) 8 6.71 3.63
Severe (20) 2 1 0.000 0.002\*
S.D ± 2.49 ± 1.69 *t* = -2.30, 0.01\*
N Mean S.D
Mild (18) 24 8.52 3.70
Normal (11) 12 12.18 4.14
*P* value for t-test of equality of means\* \*\*
------------------------------------------------------------------------------------------------------------------------------------------------------------------------------
CST-QOL: The scores range from 1 to 5, with 5 meaning no limitation and 1 meaning an extreme limitation in daily living activities.
######
Comparison of mean scores on the two versions of the CST-QOL by gender of patient
-----------------------------------------------------------------------------------------------------------------------------------------------------------------------
CST-QOL (Child version) Males (21)\ Females (18)\ *t* P value
Mean ± S.D Mean ± S.D
------------------------------------------- ------------------- ------------------------------------- --------------- --------------- ------- --------- -----------
All patients (39) Units Adult version Child version *t* P value
Number Mean ± S.D Number Mean ± S.D
[Table 2](#T2){ref-type="table"} (*All*) 12.10 ± 3.86 Males (21) 9.67 ± 4.52 8.22 ± 2.54 1.16 0.12 0.41\
0.49
Mean S.D
All Mean ± S.D (*t* = -1.59, 0.12) (*t* = -2.04, 0.05) Females (18) 10.00 ± 3.76 5.57 ±
Patients 11.00 ± 3.93 8.44 ± 3.31 4.17 4.50
Mean S.D
Males Mean ± S.D (*t* = -1.68, 0.09) (*t* = -2.16, 0.04) (t = -1.78, 0.09) 8.22 ± 4.52 4.07 ± 4.34
2.11 1.97
All Mean ± S.D Females (18)
CST-QOL 10.00 ± 3.76 (*t* = -1.39, 0.18) (*t* = -2.21, 0.04) (*t* = -1.54, 0.13) 5.57 ± 4.50 3.22 ± 4.03
Mean S.D
(*t* = -1.35, 0.18) 5.48 ± 3.55 (*t* = -2.04, 0.05) (*t* = -2.10, 0.04) 4.04 ± 3.50
Mean S.D
FSHD: Patients
(*t* = -1.78, 0.09) 2.11 ± 1.96 1.67 ± 1.67 0.001\*\
2.17 ± 1.91
(*t* = -2.21, 0.04) 2.08 ± 2.00
Mild (20) Mean ± S.D (*t* = -1.69, 0.09) (*t* = -2.01, 0.06) (*t* = -2.11, 0.04) Mean S.D (*t* = -1.52, 0.14) 8.00 ± 4.14 4.27 ± 4.05 0.002\*
FSHD: Patients 11.80 ± 3.71 8.89 ± 3.27 (*t* = -1.30, 0.20) 5.52 ± 4.30 3.22 ± 4.43
Males 10.42 ± 3.78 (*t* = -1.73, 0.10) (*t* = -2.19
